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Praça Dom Feliciano 39 sala 1.401 - Centro Histórico - Porto Alegre - RS - Brasil
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rafael . neurocirurgia@gmail.com
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(51) 3085.2695
Dr. Rafael Oliveira
Especialista em Neurocirurgia e Cirurgia de Coluna Vertebral
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DISTROFIA MUSCULAR DE DUCHENNE
Herança recessiva ligada ao X que afeta tipicamente o sexo masculino. O inicio se dá antes dos 5 anos de idade caracterizado por retardo do desenvolvimento neuropsicomotor. A fraqueza muscular proximal é progressiva. O nível de CK está elevado, a ENMG está alterada e o diagnóstico é confirmado com a ausência de distrofina (proteína muscular) na biópsia do músculo. O uso de prednisona (0,75mg/kg/dia) pode aumentar a força muscular e prolongar a deambulação até os 3 anos de idade.
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